Olmsted syndrome.
Artigo
em Inglês
| IMSEAR
| ID: sea-1216
ABSTRACT
Olmsted syndrome is a rare disorder characterized by symmetrical sharply marginated mutilating keratoderma of palms & soles & hyperkeratotic plaques around the body orifices, onychodystrophy, ainhum & amputation of digital phalanges, flextion deformities of the fingers, localized alopecia, leukokeratosis of the tongue, shortness of stature & laxity of large joints. Inheritance is autosomal dominant, although sporadic cases have been reported. Here we describe two cases of this rare disorder with thickened hyperkeratotic lesion over palm & soles & along with amputation of 3rd , 4th & 5th toes in one case. In one of our case (case no. 2) the immediate younger brother has got the same disease. Both of them were treated with tab. Neotegason 25 mg orally daily for 3 months & there was significant improvement after treatment.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Pele
/
Síndrome
/
Anormalidades Congênitas
/
Feminino
/
Humanos
/
Masculino
/
Adolescente
/
Ceratodermia Palmar e Plantar
/
Adulto
/
Instabilidade Articular
Idioma:
Inglês
Ano de publicação:
2007
Tipo de documento:
Artigo
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