Extrahepatic portal hypertension due to familial protein S deficiency.
Indian Pediatr
;
2009 Jan; 46(1): 70-1
Artigo
em Inglês
| IMSEAR
| ID: sea-12211
ABSTRACT
Portal vein thrombosis (PVT) is a common cause of portal hypertension in children. A majority of children with PVT of unknown etiology have functional Protein C deficiency or abnormally elevated levels of anti-cardiolipin antibodies. We report an 8 years old Indian girl with portal cavernoma due to hereditary Protein S deficiency. We documented familial deficiency of Protein S in 2 asymptomatic siblings suggesting that this deficiency is the primary cause of portal vein thrombosis.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Veia Porta
/
Feminino
/
Humanos
/
Criança
/
Deficiência de Proteína S
/
Trombose Venosa
/
Hipertensão Portal
Idioma:
Inglês
Revista:
Indian Pediatr
Ano de publicação:
2009
Tipo de documento:
Artigo
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