Mucous membrane pemphigoid with antibodies against β3 subunit of laminin-332: First report from India.
Indian J Dermatol Venereol Leprol
;
2012 Jul-Aug; 78(4): 475-479
Artigo
em Inglês
| IMSEAR
| ID: sea-141134
ABSTRACT
Mucous membrane pemphigoid (MMP) is a chronic, recurrent, progressive, subepidermal blistering disorder, mainly affecting the mucous membranes. Anti-laminin 332 MMP is a distinct subset of MMP with antibodies, mainly targeted against α3 or γ2 subunit. Antibodies exclusively against β3 subunit are rarely seen. An internal malignancy is frequently associated with anti-laminin 332 MMP. This disorder usually responds poorly to treatment, requiring multidisciplinary approach. Herein, we describe the first case of anti-laminin-332 MMP from India, which showed antibodies exclusively to β3 subunit.
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DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Idioma:
Inglês
Revista:
Indian J Dermatol Venereol Leprol
Ano de publicação:
2012
Tipo de documento:
Artigo
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