Wegener's granulomatosis mimicking paraneoplastic syndrome.
Indian J Chest Dis Allied Sci
;
2008 Jul-Sep; 50(3): 295-7
Artigo
em Inglês
| IMSEAR
| ID: sea-29765
ABSTRACT
Wegener's granulomatosis is a distinct clinico-pathological entity characterised by a triad of upper and lower respiratory disease and renal involvement, although atypical presentations can be seen. These patients characteristically have small vessel vasculitis and or granulomatous vasculitis and are usually anti-neutrophilic cytoplasmic antibody (ANCA) positive. We present a case of Wegener's granulomatosis that clinically mimicked a lung neoplasm with a paraneoplastic syndrome. Biopsy and histopathological evaluation of a readily accessible subcutaneous nodule showed small vessel vasculitis. Correlation with clinical data and ANCA positivity led to a definite diagnosis.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Síndromes Paraneoplásicas
/
Feminino
/
Humanos
/
Granulomatose com Poliangiite
/
Diagnóstico Diferencial
/
Neoplasias Pulmonares
/
Pessoa de Meia-Idade
Tipo de estudo:
Estudo diagnóstico
Idioma:
Inglês
Revista:
Indian J Chest Dis Allied Sci
Ano de publicação:
2008
Tipo de documento:
Artigo
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