Embryonic testicular regression syndrome: a case report.
Artigo
em Inglês
| IMSEAR
| ID: sea-38224
ABSTRACT
A case of testicular regression syndrome was reported. The patient was an 18 year old girl presenting with primary amenorrhoea. Physical examination revealed normal female external genitalia and underdeveloped secondary sexual characteristics. Hormonal profile indicated gonadal failure. Chromosome analysis revealed 46,XY karyotype. Diagnostic laparoscopy demonstrated undeveloped internal genital organs. Remnants of epididymis, vas deferens and seminiferous tubule were uncovered during exploratory laparotomy. Ontogeny of sexual differentiation and pathogenesis of testicular regression syndrome were reviewed and discussed.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Síndrome de Resistência a Andrógenos
/
Feminino
/
Humanos
/
Masculino
/
Adolescente
/
Amenorreia
Idioma:
Inglês
Ano de publicação:
1999
Tipo de documento:
Artigo
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