Syndrome of progressive ataxia and palatal myoclonus: a case report.
Artigo
em Inglês
| IMSEAR
| ID: sea-42219
ABSTRACT
A 46-year old man presented with progressive cerebellar ataxia for 5 years. Physical examination revealed palatal and tongue myoclonus, cerebellar gait, limb ataxia and spasticity of the lower extremities. The imaging studies including CT-scan and MRI of the brain revealed progressive pancerebellar atrophy and bilateral hypertrophic degeneration of inferior olives. The clinical course was slowly progressive. Various medications included anticonvulsants, benzodiazepines and antispasticity failed to abolish the abnormal palatal movement and ataxic syndrome. The syndrome of progressive ataxia and palatal myoclonus is a rare and unique neurodegenerative syndrome. The pathogenesis and treatment are still unknown.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Síndrome
/
Humanos
/
Masculino
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Tomografia Computadorizada por Raios X
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Ataxia Cerebelar
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Progressão da Doença
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Adulto
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Mioclonia
Idioma:
Inglês
Ano de publicação:
1999
Tipo de documento:
Artigo
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