Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS): a case report in Thailand.
Artigo
em Inglês
| IMSEAR
| ID: sea-45158
ABSTRACT
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a rare congenital disease with high mortality rate. The authors report a case of a female term infant with massive abdominal distension at birth. Abdominal ultrasonography revealed a huge cystic mass resolved after urinary catheterization. Exploratory laparotomy was performed and intraoperative findings were an enlarged urinary bladder, microcolon, short bowel and malrotation of the small intestine. Ladd's procedure, ileostomy and vesicostomy were performed. Pathological findings of rectal biopsy revealed normal ganglion cells. Although prokinetic drugs were given for promoting bowel motility, enteral feedings were not tolerated. She died from septicemia at the age of 50 days.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Peristaltismo
/
Síndrome
/
Tailândia
/
Anormalidades Múltiplas
/
Bexiga Urinária
/
Feminino
/
Humanos
/
Recém-Nascido
/
Colo
País/Região como assunto:
Ásia
Idioma:
Inglês
Ano de publicação:
2004
Tipo de documento:
Artigo
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