Papillon-Lefevre syndrome: two case reports.
Artigo
em Inglês
| IMSEAR
| ID: sea-51876
ABSTRACT
Papillon-Lefevre syndrome is a rare autosomal recessive disorder in which there is palmoplantar keratinization and premature loss of both deciduous and permanent teeth. The palmoplantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at the age of 3 or 4 years. An early diagnosis of the syndrome can help preserve the teeth by early institution of treatment, using a multidisciplinary approach. We present two cases of the syndrome having all of the characteristic features.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Doença de Papillon-Lefevre
/
Periodontite
/
Esfoliação de Dente
/
Feminino
/
Humanos
/
Masculino
/
Perda do Osso Alveolar
/
Adolescente
/
Gengivite
Tipo de estudo:
Estudo de rastreamento
Idioma:
Inglês
Ano de publicação:
2007
Tipo de documento:
Artigo
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