Reversal of severe hepato-pulmonary syndrome in congenital hepatic fibrosis after living-related liver transplantation.
Artigo
em Inglês
| IMSEAR
| ID: sea-65122
ABSTRACT
We report a 5-year-old girl with congenital hepatic fibrosis who presented with clubbing and cyanosis. Partial pressure of oxygen was 40 mmHg with oxy-gen saturation of 70% on room air, which improved to 128 mmHg and 92% on inhalation of 100% oxygen. Macroaggregated albumin scan showed 58% shunting to the brain, suggestive of severe hepatopulmonary syndrome. Echocardiogram and pulmonary angiogram ruled out pulmonary hypertension. Four weeks after living-related liver transplantation, she had normal blood gases and reduction in shunting to 7% on macroaggregated albumin scan.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Feminino
/
Humanos
/
Pré-Escolar
/
Agregado de Albumina Marcado com Tecnécio Tc 99m
/
Seguimentos
/
Transplante de Fígado
/
Resultado do Tratamento
/
Doadores Vivos
/
Síndrome Hepatopulmonar
/
Cirrose Hepática
Tipo de estudo:
Estudo observacional
/
Estudo prognóstico
/
Fatores de risco
Idioma:
Inglês
Ano de publicação:
2007
Tipo de documento:
Artigo
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