Achalasia--alacrima--ACTH insensitivity syndrome (Triple A syndrome).
Indian J Pediatr
;
2003 Apr; 70(4): 343-5
Artigo
em Inglês
| IMSEAR
| ID: sea-79988
ABSTRACT
Triple A syndrome is characterized by achalasia of the cardia, alacrima, adrenocorticotrophic hormone (ACTH) resistant adrenal insufficiency and progressive neurological abnormalities including autonomic nervous dysfunction. An 8-year-old girl presented to the pediatric intensive care unit with sudden loss of consciousness and was diagnosed subsequently to have this condition. The authors present this condition since it is easily treatable and can be fatal if undiagnosed.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Linhagem
/
Síndrome
/
Sulfato de Bário
/
Feminino
/
Humanos
/
Masculino
/
Acalasia Esofágica
/
Criança
/
Pré-Escolar
/
Resultado do Tratamento
Idioma:
Inglês
Revista:
Indian J Pediatr
Ano de publicação:
2003
Tipo de documento:
Artigo
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