Hereditary factor XIII deficiency.
Indian J Pediatr
;
1993 May-Jun; 60(3): 441-4
Artigo
em Inglês
| IMSEAR
| ID: sea-81854
ABSTRACT
Twelve cases of hereditary factor XIII (FX III) deficiency diagnosed over five years (1986-1990) at Christian Medical College and Hospital, Vellore are presented here. Although all the cases had a history of umbilical cord bleeding and subsequent frequent bleeding episodes, diagnosis was considerably delayed. All but two patients required transfusions for bleeding episodes. Ten patients had a history of consanguinity in parents. Clinical features and family history are described in detail here. The ease of performing the Urea solubility test and problems in it's interpretation are highlighted. The role of prophylactic transfusion is also discussed.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Plasma
/
Testes de Coagulação Sanguínea
/
Transfusão de Sangue
/
Feminino
/
Humanos
/
Masculino
/
Fator XIII
/
Recém-Nascido
/
Criança
/
Pré-Escolar
Idioma:
Inglês
Revista:
Indian J Pediatr
Ano de publicação:
1993
Tipo de documento:
Artigo
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