Congenital factor XIII deficiency: two case reports.
Artigo
em Inglês
| IMSEAR
| ID: sea-86917
ABSTRACT
Two patients with factor XIII deficiency, presenting with bleeding disorder since birth, are reported. The condition is rare and is likely to be missed unless clot solubility in 5 M urea is performed as a screening test in all patients with bleeding disorders. A correct diagnosis is essential as prophylactic management is practicable in this disorder.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Testes de Coagulação Sanguínea
/
Humanos
/
Masculino
/
Criança
/
Adulto
/
Deficiência do Fator XIII
Idioma:
Inglês
Ano de publicação:
1991
Tipo de documento:
Artigo
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