Rosai Dorfman disease--a clinico-pathological presentation.
Artigo
em Inglês
| IMSEAR
| ID: sea-91116
ABSTRACT
Rosai Dorfman disease (RDD) or sinus histiocytosis with massive lymphadenopathy (SHML) is a rare disorder that typically manifests as lymphadenopathy and systemic symptoms. The authors report a 45 year old lady who presented with nasal mass and generalised lymphadenopathy. Histopathological examination demonstrated lymphophagocytosis (emperipolesis) consistent with a diagnosis of RDD. The clinical and histologic aspects of the disease are discussed as a rare cause of generalised lymphadenopathy.
Texto completo:
DisponíveL
Índice:
IMSEAR (Sudeste Asiático)
Assunto principal:
Feminino
/
Humanos
/
Histiocitose Sinusal
/
Doenças Linfáticas
/
Pessoa de Meia-Idade
Idioma:
Inglês
Ano de publicação:
2007
Tipo de documento:
Artigo
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