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Intravenous Leiomyomatosis with Extension to the Heart Associated with Disseminated Peritoneal Leiomyomatosis / 대한내과학회지
Korean Journal of Medicine ; : 185-190, 2016.
Artigo em Coreano | WPRIM | ID: wpr-101518
ABSTRACT
Leiomyomatosis refers to benign smooth muscle cell tumors that often arise from unusual growth patterns and include benign metastasizing leiomyoma, disseminated peritoneal leiomyomatosis, and intravenous leiomyomatosis. Intravenous leiomyomatosis is the extension of a vascular tumor into the venous channels, whereas disseminated peritoneal leiomyomatosis is characterized by multiple leiomyomas growing along the submesothelial tissues of the abdominopelvic peritoneum. It is extremely rare for intravenous leiomyomatosis and disseminated peritoneal leiomyomatosis to occur simultaneously. A 42-year-old female presented with disseminated peritoneal leiomyomatosis and intravenous leiomyomatosis extended through the inferior vena cava into the right side of the heart. The patient underwent one-stage surgery under simultaneous sternotomy and laparotomy, and radical excision of the tumor was achieved using cardiopulmonary bypass. Here we describe a case in which complete removal of a leiomyomatosis with an unusual growth pattern was successfully performed using one-stage surgery.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Peritônio / Veia Cava Inferior / Ponte Cardiopulmonar / Leiomiomatose / Miócitos de Músculo Liso / Esternotomia / Coração / Laparotomia / Leiomioma Limite: Adulto / Feminino / Humanos Idioma: Coreano Revista: Korean Journal of Medicine Ano de publicação: 2016 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Peritônio / Veia Cava Inferior / Ponte Cardiopulmonar / Leiomiomatose / Miócitos de Músculo Liso / Esternotomia / Coração / Laparotomia / Leiomioma Limite: Adulto / Feminino / Humanos Idioma: Coreano Revista: Korean Journal of Medicine Ano de publicação: 2016 Tipo de documento: Artigo