A Case of Malignant Extrarenal Rhabdoid Tumor
Journal of the Korean Pediatric Society
;
: 1292-1297, 1999.
Artigo
em Coreano
| WPRIM
| ID: wpr-102233
ABSTRACT
Malignant Rhabdoid tumor is a rare malignant neoplasm and is morphologically similar to rhabdomyosarcoma, but is different immunohistochemically. Most malignant rhabdoid tumors occur in the kidney of infants, and are rarely reported at extrarenal sites. Since Frierson and his collagues first described the malignant extrarenal rhabdoid tumor(MRT) in children in 1985, it has rarely been reported. The neoplasm is histologically and immunohistochemically identical to a renal malignant rhabdoid tumor. There have been no previous reports of this neoplasm in Korea. An MRT of the sacroiliac bone in a 11-year-old girl is described. Five months after the initial presentation, the patient is still alive with partial response to combination chemotherapy and radiotherapy. The authors review previous reports of extrarenal MRT, and discuss the pathologic characteristics, differential diagnosis, and treatment of this rare neoplasm.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Radioterapia
/
Rabdomiossarcoma
/
Tumor Rabdoide
/
Diagnóstico Diferencial
/
Quimioterapia Combinada
/
Rim
/
Coreia (Geográfico)
Tipo de estudo:
Estudo diagnóstico
Limite:
Criança
/
Feminino
/
Humanos
/
Lactente
País/Região como assunto:
Ásia
Idioma:
Coreano
Revista:
Journal of the Korean Pediatric Society
Ano de publicação:
1999
Tipo de documento:
Artigo
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