Epitheloid Sarcoma in the Hand: A Case Report

ABSTRACT

Epitheloid sarcoma is rare malignant tumor of the skin, connective tissue, subcutaneous tissue and tendon sheath, which was first described by Enzinger in 1970. It is usually located in the extremities. We treated a 30-years-old man who developed an epitheloid sarcoma in the radial side of the left palm. The tumor was 2x1.6x1 cm sized, arose from the thenar muscle, and histologically the mass was composed of epitheloid cells. It was treated by wide local excision. However, after 2 months of initial operation, second operation and radiotheraphy was performed because of local recurrence. Because of its harmless appearance and similarity to an inflammatory response, it is often mistaken for a benign lesion.Even though it is a rare tumor, clinicians and pathologists should be aware of this malignant nature. Metastasis can be local or may involve draining lymph node and other distant organs, mostly the lung. Diagnosis is made on pathologic evaluation. Aggressive surgical approach is required in order to prevent recurrence, and radiotherapy and chemotherapy should be considered in all cases.