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Febrile Ulceronecotic Pityriasis Lichenoides et Varioliformis Acuta Successfully Treated with Oral Cyclosporin / 대한피부과학회지
Korean Journal of Dermatology ; : 565-568, 2012.
Artigo em Inglês | WPRIM | ID: wpr-106450
ABSTRACT
Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta (PLEVA), or febrile ulcerative Mucha-Haberman disease (FUMHD) is very rare, but potentially lethal variants of PLEVA. This subtype is characterized by rapidly progressive ulceronecrotic lesions and systemic manifestations, such as high fever, gastrointestinal, neurological, cardiologic and pulmonary involvement, and rheumatologic manifestations. Several treatments with variable response have been challenged, such as systemic steroid, antibiotics, methotrexate, dapsone, cyclosporine and ultraviolet therapy. But there is no standard therapy for FUMHD to date. We report a 59-year-old woman with FUMHD, who recurred after discontinuation of systemic steroid, but successfully treated with oral cyclosporine.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Pitiríase / Úlcera / Terapia Ultravioleta / Metotrexato / Ciclosporina / Pitiríase Liquenoide / Dapsona / Febre / Antibacterianos Limite: Feminino / Humanos Idioma: Inglês Revista: Korean Journal of Dermatology Ano de publicação: 2012 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Pitiríase / Úlcera / Terapia Ultravioleta / Metotrexato / Ciclosporina / Pitiríase Liquenoide / Dapsona / Febre / Antibacterianos Limite: Feminino / Humanos Idioma: Inglês Revista: Korean Journal of Dermatology Ano de publicação: 2012 Tipo de documento: Artigo