A Case of Dissection in Marfan Syndrome with Ascending Aortic Aneurysm / 영남의대학술지
Yeungnam University Journal of Medicine
;
: 179-184, 1989.
Artigo
em Coreano
| WPRIM
| ID: wpr-108846
ABSTRACT
The Marfan syndrome is a generalized connective tissue disease involving eye, musculoskeletal system, cardiovascular system, and inherited autosomal dominant with various expression type. The cardiovascular complications such as aortic aneurysm, aortic dissection, aortic regurgitation, mitral regurgitation and aortic dissection which usually occurs in previously normal sized aorta are poor prognostic factors. However, the aortic dissection which developed in patient with Marfan syndrome and aortic aneurysm was rare. We experienced one case of dissecting aneurysm in patient diagnosed as previous aortic aneurysm, aortic regurgitation, and Marfan syndrome, receiving successful operation.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Aorta
/
Aneurisma Aórtico
/
Insuficiência da Valva Aórtica
/
Sistema Cardiovascular
/
Doenças do Tecido Conjuntivo
/
Dissecção Aórtica
/
Síndrome de Marfan
/
Insuficiência da Valva Mitral
/
Sistema Musculoesquelético
Tipo de estudo:
Estudo prognóstico
Limite:
Humanos
Idioma:
Coreano
Revista:
Yeungnam University Journal of Medicine
Ano de publicação:
1989
Tipo de documento:
Artigo
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