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A Case of Becker Muscular Dystrophy Associated With Dilated Cardiomyopathy / 대한내과학회지
Korean Journal of Medicine ; : 708-711, 1997.
Artigo em Coreano | WPRIM | ID: wpr-111783
ABSTRACT
Dilated cardiomyopaty is a rare occurrence in Hecker muscular dystropy. We report a case of Becken muscular dystrophy in 28 old man who presented with dyspnea, progressive muscle weakness, and dilated cardiomyopathy with severe left ventricular dysfunction which was detected by echocardiograpy. Muscle biopsy demonstrated diffuse degenerated changes consistent with progressive muscular dystropy, His brother has also Becker muscular dystrophy and dilated cardiomyopathy, The patient is on NYHA Class II~III with medical therapy.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Biópsia / Cardiomiopatia Dilatada / Disfunção Ventricular Esquerda / Debilidade Muscular / Distrofia Muscular de Duchenne / Irmãos / Dispneia / Distrofias Musculares Limite: Humanos Idioma: Coreano Revista: Korean Journal of Medicine Ano de publicação: 1997 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Biópsia / Cardiomiopatia Dilatada / Disfunção Ventricular Esquerda / Debilidade Muscular / Distrofia Muscular de Duchenne / Irmãos / Dispneia / Distrofias Musculares Limite: Humanos Idioma: Coreano Revista: Korean Journal of Medicine Ano de publicação: 1997 Tipo de documento: Artigo