Living Donor Liver Transplantation for an Infant with Osteogenesis Imperfecta and Intrahepatic Cholestasis: Report of a Case
Journal of Korean Medical Science
;
: 441-444, 2014.
Artigo
em Inglês
| WPRIM
| ID: wpr-111999
ABSTRACT
Osteogenesis imperfecta (OI) is a group of genetic disorders characterized by bone fragility and connective tissue manifestations. We report a successful liver transplantation (LT) in an 8-month-old boy with OI and cholestatic biliary cirrhosis. After 4 cycles of intravenous pamidronate, LT was performed under intravenous anesthesia using a left lateral section from his mother without mechanical retractors. The operation time was 420 min and estimated blood loss was 520 mL requiring one unit of RBC transfusion. He was discharged without surgical complications. Therefore, LT should be considered for patients with end stage liver disease and OI under organic multidisciplinary cooperation.
Texto completo:
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Índice:
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Assunto principal:
Osteogênese Imperfeita
/
Densidade Óssea
/
Colestase Intra-Hepática
/
Transplante de Fígado
/
Doadores Vivos
/
Difosfonatos
/
Fraturas Ósseas
/
Conservadores da Densidade Óssea
Limite:
Humanos
/
Lactente
/
Masculino
Idioma:
Inglês
Revista:
Journal of Korean Medical Science
Ano de publicação:
2014
Tipo de documento:
Artigo
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