A Case of Repeated Ventricular Tachycardia Caused by Cardiac Rhabdomyomas in an Infant with Tuberous Sclerosis
Journal of the Korean Pediatric Society
;
: 913-917, 2003.
Artigo
em Coreano
| WPRIM
| ID: wpr-112016
ABSTRACT
Cardiac rhabdomyomas are relatively uncommon and associated with tuberous sclerosis in 40-50% cases. We report a 10-month-old infant with tuberous sclerosis who presented with ventricular arrythmias and status epilepticus. There were hypopigmented macules on the body, periventricular calcifications, renal cyst and cardiac rabdomyomas just below the aortic valve. The patient required resection of left ventricular subaortic masses due to sustained arrythmia in spite of intravenous amiodarone therapy. The pathologic examination confirmed the diagnosis of rhabdomyoma. The patient had no more arrythmia during the 14 month follow up period. Although cardiac rhabdomyomas may spontaneously regress, surgery is often necessary and frequently resolves the underlying arrythmia.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Valva Aórtica
/
Arritmias Cardíacas
/
Rabdomioma
/
Estado Epiléptico
/
Esclerose Tuberosa
/
Seguimentos
/
Taquicardia Ventricular
/
Diagnóstico
/
Amiodarona
Tipo de estudo:
Estudo diagnóstico
/
Estudo observacional
/
Estudo prognóstico
Limite:
Humanos
/
Lactente
Idioma:
Coreano
Revista:
Journal of the Korean Pediatric Society
Ano de publicação:
2003
Tipo de documento:
Artigo
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