A Case of Clear Cell Sarcoma with Inguinal Lymph Node Metastasis / 대한피부과학회지

ABSTRACT

Clear cell sarcoma is a rare malignant soft tissue tumor, a well accepted clinicopathological entity of malignant melanoma of soft parts. It mainly affects young adults with a predominance in women. The predilection sites are extremities, especially foot and ankle. We report a case of clear cell sarcoma with inguinal lymph node metastasis in a 26-year-old woman. She had a deep seated nodule on her left anterior thigh for 4 years along with lymphadenopathy for 2 months at the initial presentation. Histopathologic findings displayed a uniform pattern of compact nests or fascicles of round or fusiform cells showing clear cytoplasm and vesicular nuclei. Total removal of the original mass, lymphadenectomy, adjuvant radiation and chemotherapy with dacarbazine were performed. To date, no recurrence has been observed during a 1 year- follow up period.