Myasthenia in Acquired Neuromyotonia
Journal of Clinical Neurology
; : 69-71, 2014.
Article
em En
| WPRIM
| ID: wpr-113288
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WPRO
ABSTRACT
BACKGROUND: Acquired neuromyotonia (NMT) forms part of the spectrum of acquired peripheral nerve hyperexcitability syndrome, and is thought to be caused by antibodies to voltage-gated potassium channels (VGKC). Exertional weakness is unusual unless autoimmune myasthenia gravis (MG) is superimposed. CASE REPORT: A case of acquired NMT accompanied by exertional weakness without coexistence of seropositive MG is reported herein. CONCLUSIONS: Clinical and electrophysiological observations suggest that the cholinergic overactivity in NMT can compromise the safety factor sufficiently to cause a defect in neuromuscular junction transmission.
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Assunto principal:
Nervos Periféricos
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Síndrome de Isaacs
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Canais de Potássio de Abertura Dependente da Tensão da Membrana
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Anticorpos
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Miastenia Gravis
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Junção Neuromuscular
Idioma:
En
Revista:
Journal of Clinical Neurology
Ano de publicação:
2014
Tipo de documento:
Article