A Case of Pigmented Paravenous Retino-Choroidal Atrophy and Retinitis Pigmentosa

ABSTRACT

Pigmented paravenous retinochoroidal atrophy(PPRCA) is an uncommon disease that was first reported in 1937 by T.H.Brown. The diagnosis was based on the distinctive fundus appearance of bone corpuscular pigment accumulation, exclusively along the distribution of the retinal vein. Depending on the degree of severity, there may be peripapillary changes, as well as areas of chrioretinal atrophy adjacent to the perivenular pigmentary changes. Although the fundus abnormalities can be mild or severe, retinal function tests indicated that this is geographic and not a generalized disorder. We experienced a case of PPRCA in the left eye a 40 year-old male, which was associated with retinitis pigmentosa in his right eye.