A Case of Complete Remission of Hairy Cell Leukemia by 2-Chlorodeoxyadenosine / 영남의대학술지
Yeungnam University Journal of Medicine
;
: 237-241, 2004.
Artigo
em Coreano
| WPRIM
| ID: wpr-121425
ABSTRACT
Hairy cell leukemia (HCL) is an uncommon chronic B-cell lymphoproliferative disorder that is characterized by cytopenia, splenomegaly, and mononuclear cells displaying cytoplasmic projections. We experienced a case of hairy cell leukemia that developed in a 38-year-old man. He showed marked splenomegaly without palpable lymphoadenopathy. A complete blood cell count revealed leukopenia (3300/microliter with 63% of lymphocyte) and the peripheral blood smear showed abnormal lymphoid cells with cytoplasmic projections. The bone marrow smear revealed abnormal lymphocytes and severe myelofibrosis. Tartrate-resistant acid phosphatase reactivity was strongly positive in the hairy cells. The immunophenotyping results of lymphoid cells were CD5 (-), CD10 (-), CD19 (+), CD25 (+), CD103 (+), CD20 (+), lambda (+). The patient was treated with 2-Chlorodeoxyadenosine at a daily dose of 0.1mg/Kg by a continuous intravenous infusion for 7 days. The patient achieved complete remission.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Esplenomegalia
/
Fosfatase Ácida
/
Contagem de Células Sanguíneas
/
Medula Óssea
/
Infusões Intravenosas
/
Linfócitos B
/
Linfócitos
/
Leucemia de Células Pilosas
/
Imunofenotipagem
/
Cladribina
Limite:
Adulto
/
Humanos
Idioma:
Coreano
Revista:
Yeungnam University Journal of Medicine
Ano de publicação:
2004
Tipo de documento:
Artigo
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