A Case of Febrile Ulceronecrotic Mucha-Habermann's Disease in an Infant / 대한피부과학회지

ABSTRACT

Febrile ulceronecrotic Mucha-Habermann's disease (FUMHD) is an unusual severe form of pityriasis lichenoides et varioliformis acuta (PLEVA) characterized by abrupt onset of widespread ulceronecrotic cutaneous eruption associated with high fever and systemic symptoms. In most cases, a mild typical form of PLEVA was usually present prior to the acute fulminating course. We report a case of FUMHD in a 6-month-old infant, who presented widespread hemorrhagic papules and coalescent thickly crusted ulcerations, high fever, liver dysfunction, and diarrhea with histopathologic findings suggestive of PLEVA.