Desmoplastic Small Round Cell Tumor: Radiologic Findings

ABSTRACT

PURPOSE: To evaluate the radiologic findings of intra-abdominal DSRCT. MATERIALS AND METHODS: We reviewed sixcases of pathologically proven DSRCT of the abdomen. Five of these patients were men and one was a woman ; theiraverage age was 26.8 years. We retrospectively analyzed CT(n=6) and MRI(n=4). RESULTS: In all patients, largerelatively well defined lobulated mass was seen;this arose from the peritoneal surface, and its average size was12.6(range, 10-18)cm. After the administration of contrast material, the masses showed inhomogeneous enhancement,and in addition, the following features were seen irregular internal septations (n=5); necrosis (n=3); andamorphous calcification (n=4). Various associated findings such as ascites (n=4) and multiple para-aortic lymphnode enlargement (n=4) were present; omental cake (n=5), liver metastasis (n=1), cervical lymphadenopathy (n=1),hydronephrosis (n=1), small bowel obstruction (n=1), scrotal swelling (n=1) and collateral vessels by encasedaorta and renal vein (n=1) were also seen. CONCLUSION: In young male patients with a large heterogeneous enhaneedcalcified abdominopelvic mass and findings of carcinomatosis on both CT and MR images, DSRCT should be inelvded inthe differential diagnosis.