A Case of Congenital Disseminated Malignant Rhabdoid Tumor of the Soft Tissue in Neonate / 대한주산의학회잡지
Korean Journal of Perinatology
; : 311-316, 2010.
Article
em Ko
| WPRIM
| ID: wpr-130993
Biblioteca responsável:
WPRO
ABSTRACT
Malignant rhabdoid tumor (MRT) was first described as a "rhabdomyosarcomatoid" variant of Wilms tumor, but was later identified as a distinct entity. MRTs are extremely rare and highly aggressive neoplasm with poor outcome, occurring mostly in kidneys and central nervous system, less frequently in extrarenal sites. MRTs are referred to as "congenital" when it is diagnosed at or immediately after birth. There are few reports about congenital disseminated MRT at birth. We report a case of congenital malignant rhabdoid tumor presenting as a soft tissue mass in the right arm at birth although the autopsy revealed the systemic disseminated tumors through the whole body with typical microscopic findings.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Braço
/
Autopsia
/
Sistema Nervoso Central
/
Tumor Rabdoide
/
Tumor de Wilms
/
Parto
/
Rim
Tipo de estudo:
Prognostic_studies
Limite:
Humans
/
Newborn
Idioma:
Ko
Revista:
Korean Journal of Perinatology
Ano de publicação:
2010
Tipo de documento:
Article