A Case of General Congenital Fibrosis Syndrome With A-pattern Strabismus
Journal of the Korean Ophthalmological Society
;
: 2021-2026, 2008.
Artigo
em Coreano
| WPRIM
| ID: wpr-132884
ABSTRACT
PURPOSE:
To report a case of general congenital fibrosis syndrome with A-pattern strabismus, bilateral ptosis and hypotropia. CASESUMMARY:
A six-year-old girl was presented with severe bilateral ptosis and esodeviation of the left eye since birth. No levator action was presented and her chin was elevated at an angle of 25 degrees. In both eyes, an abduction defect was observed, and no vertical movement was presented. There was a left esotropia of 20 prism diopters (PD) and bilateral hypotropia of 35PD. There was an A-pattern strabismus that presents convergence movements during attempts to look upward, and orthotropia during attempts to look downward. Diagnosed as general congenital fibrosis syndrome with A-pattern esotropia, bilateral ptosis and hypotropia, bilateral inferior rectus muscle recessions were performed. After the operation, chin elevation and hypotropia in both eyes were corrected and exodeviation increased. Thus, orthotropia was observed in the primary position, and an A-pattern strabismus occurred with an exotropia of 15PD on the downgaze.CONCLUSIONS:
A congenital fibrosis syndrome with an A-pattern strabismus was reported for the first time by the authors. On decisions concerningsurgical amounts of horizontal deviation, exodeviation should be considered to increase after bilateral inferior rectus muscle recessions.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Fibrose
/
Esotropia
/
Exotropia
/
Estrabismo
/
Queixo
/
Parto
/
Olho
/
Músculos
Idioma:
Coreano
Revista:
Journal of the Korean Ophthalmological Society
Ano de publicação:
2008
Tipo de documento:
Artigo
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