A Cases of Adult Onset Still's Disease with Hemolytic Anemia
Journal of Rheumatic Diseases
;
: 104-107, 2012.
Artigo
em Coreano
| WPRIM
| ID: wpr-135253
ABSTRACT
Adult onset Still's disease (AOSD) is a systemic inflammatory disorder of unknown etiology. AOSD is characterized by fever, arthralgia, salmon-colored skin rash, hepatosplenomegaly and its laboratory abnormalities include leukocytosis, elevated liver enzyme, negative autoantibody, and hyperferritinemia. The clinical course varied and severe complicated conditions, such as hemophagocytic syndrome, and disseminated intravascular coagulation, occurred occasionally. Such a complication is accompanied with hemolytic anemia and lead to be a fatal course. We report the first case of AOSD with hemolytic anemia, which improved with high dose steroid therapy.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Doença de Still de Início Tardio
/
Artralgia
/
Coagulação Intravascular Disseminada
/
Linfo-Histiocitose Hemofagocítica
/
Exantema
/
Febre
/
Anemia Hemolítica
/
Leucocitose
/
Fígado
Limite:
Adulto
/
Humanos
Idioma:
Coreano
Revista:
Journal of Rheumatic Diseases
Ano de publicação:
2012
Tipo de documento:
Artigo
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