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Extramedullary Hematopoiesis at the Posterior Mediastinum in Patient with Hereditary Spherocytosis: A Case Report
Article em En | WPRIM | ID: wpr-13789
Biblioteca responsável: WPRO
ABSTRACT
Thoracic extramedullary hematopoiesis (EMH) is a rare disease entity that is usually associated with hematologic disorders, such as myelodysplastic or hemolytic disease. Because thoracic EMH is usually encountered as a mass during radiologic examinations, it should be differentiated from posterior mediastinal neurogenic tumors. Here, the authors report a case of EMH associated with hereditary spherocytosis. The patient underwent a complete excision by thoracoscopic surgery to differentiate it from other mediastinal tumors.
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Texto completo: 1 Índice: WPRIM Assunto principal: Esferocitose Hereditária / Toracoscopia / Hematopoese Extramedular / Doenças Raras / Neoplasias do Mediastino / Mediastino Limite: Humans Idioma: En Revista: The Korean Journal of Thoracic and Cardiovascular Surgery Ano de publicação: 2013 Tipo de documento: Article
Texto completo: 1 Índice: WPRIM Assunto principal: Esferocitose Hereditária / Toracoscopia / Hematopoese Extramedular / Doenças Raras / Neoplasias do Mediastino / Mediastino Limite: Humans Idioma: En Revista: The Korean Journal of Thoracic and Cardiovascular Surgery Ano de publicação: 2013 Tipo de documento: Article