A Case of Congenital Hypopituitarism with Anterior Pituitary Aplasia and Ectopic Posterior Pituitary Gland / 대한소아내분비학회지
Journal of Korean Society of Pediatric Endocrinology
;
: 174-178, 2003.
Artigo
em Coreano
| WPRIM
| ID: wpr-138140
ABSTRACT
Congenital hypopituitarism is a rare disorder with absence or reduction of hormones produced by the pituitary gland. The clinical manifestations are hypoglycemia, prolonged jaundice, hyponatremia, micropenis, underdeveloped clitoris, lethargy, convulsion, pallor, cyanosis, apnea, hypotension, temperature instability etc. in neonates and growth failure, delayed or absent puberty in older infants and children. We experienced a case of congenital hypopituitarism who was a 20-year-old male patient with short stature and delayed puberty. Combined pituitary function test revealed panhypopituitarism and magnetic resonance imaging of brain showed anterior pituitary aplasia and ectopic posterior pituitary gland.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Palidez
/
Apneia
/
Testes de Função Hipofisária
/
Hipófise
/
Neuro-Hipófise
/
Puberdade Tardia
/
Convulsões
/
Encéfalo
/
Imageamento por Ressonância Magnética
/
Puberdade
Limite:
Adolescente
/
Criança
/
Feminino
/
Humanos
/
Lactente
/
Masculino
/
Recém-Nascido
Idioma:
Coreano
Revista:
Journal of Korean Society of Pediatric Endocrinology
Ano de publicação:
2003
Tipo de documento:
Artigo
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