Weber-Christian disease presenting with proptosis: a case report
Journal of Korean Medical Science
; : 247-250, 2000.
Article
em En
| WPRIM
| ID: wpr-140416
Biblioteca responsável:
WPRO
ABSTRACT
Weber-Christian disease (WCD) is a rare inflammatory disease of adipose tissue, which is characterized by painful cutaneous nodules and constitutional symptoms. Although any area of the body containing fat can be affected by WCD, the involvement of retrobulbar fat is uncommon and proptosis is a rare presenting manifestation. We report a case who presented with proptosis of the right eye which is accompanied by painful subcutaneous nodules, high fever and myalgia. Biopsies of retrobulbar tissue and suprapubic nodule showed lobular panniculitis with mixed cellular infiltration, mainly composed of histiocytes and lymphocytes. He responded well to high-dose glucocorticoid.
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Texto completo:
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Índice:
WPRIM
Assunto principal:
Biópsia
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Imageamento por Ressonância Magnética
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Paniculite Nodular não Supurativa
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Exoftalmia
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Glucocorticoides
Limite:
Adult
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Humans
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Male
Idioma:
En
Revista:
Journal of Korean Medical Science
Ano de publicação:
2000
Tipo de documento:
Article