Non-Functioning Somatostatinoma of the Duodenum in Patient with Von Recklinghausen's Disease
Korean Journal of Hepato-Biliary-Pancreatic Surgery
; : 307-310, 2009.
Article
em En
| WPRIM
| ID: wpr-140581
Biblioteca responsável:
WPRO
ABSTRACT
Somatostatinoma is a rare endocrine tumor that comprises around 1% of all gastroenteropancreatic endocrine neoplasm. The estimated annual incidence is 1 in 40 million. This tumor may be associated with von Recklinghausen's disease. We present here a rare case of a 51-year-old female patient with a duodenal nonfunctioning somatostatinoma combined with von Recklinghausen's disease. Whipple' procedure was performed. The postoperative course was uneventful and the histopathologic findings were consistent with malignant nonfunctioning somatostatinoma with lymph node metastases. The patient is alive, healthy and without tumor recurrence 10 months after surgery.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Recidiva
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Somatostatinoma
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Incidência
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Neurofibromatose 1
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Tumores Neuroendócrinos
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Duodeno
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Linfonodos
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Metástase Neoplásica
Tipo de estudo:
Incidence_studies
/
Prognostic_studies
Limite:
Female
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Humans
Idioma:
En
Revista:
Korean Journal of Hepato-Biliary-Pancreatic Surgery
Ano de publicação:
2009
Tipo de documento:
Article