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Neonatal Lupus Erythematosus Presenting with "Eye Mask" Facial Rash and Telangiectasia / 대한피부과학회지
Korean Journal of Dermatology ; : 974-977, 2012.
Artigo em Coreano | WPRIM | ID: wpr-146771
ABSTRACT
Neonatal lupus erythematosus (NLE) is an autoimmune disease associated with the maternal anti-SSA/Ro and anti-SSB/La antibodies. NLE is characterized by cutaneous erythema, congenital heart block (CHB), hepatic dysfunction and hematological abnormalities. The characteristic cutaneous lesion is an annular or polycyclic erythematous patch or plaque. Individual annular lesions are often about 1 cm in diameter. We report a case of NLE in a 7-day-old female infant, born of a clinically asymptomatic mother, presenting "eye mask" shape rash and telangiectasia on her face. Periorbital rash with "eye mask" appearance presents in a few of NLE cases, and this cutaneous sign has been emphasized as a diagnostic clue to NLE. Her serological tests revealed high titers of anti-SSA/Ro, anti-SSB/La and antinuclear antibody. Based on these clinical and serological findings, the patient was diagnosed as NLE with characteristic periorbital skin findings.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Pele / Doenças Autoimunes / Telangiectasia / Testes Sorológicos / Anticorpos Antinucleares / Eritema / Exantema / Bloqueio Cardíaco / Lúpus Eritematoso Sistêmico / Anticorpos Tipo de estudo: Estudo diagnóstico Limite: Feminino / Humanos / Lactente Idioma: Coreano Revista: Korean Journal of Dermatology Ano de publicação: 2012 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Pele / Doenças Autoimunes / Telangiectasia / Testes Sorológicos / Anticorpos Antinucleares / Eritema / Exantema / Bloqueio Cardíaco / Lúpus Eritematoso Sistêmico / Anticorpos Tipo de estudo: Estudo diagnóstico Limite: Feminino / Humanos / Lactente Idioma: Coreano Revista: Korean Journal of Dermatology Ano de publicação: 2012 Tipo de documento: Artigo