Congenital syngnathia: a case report
Journal of the Korean Association of Oral and Maxillofacial Surgeons
;
: 171-176, 2012.
Artigo
em Inglês
| WPRIM
| ID: wpr-150775
ABSTRACT
Congenital syngnathia refers to the fusion of bony tissues, a rare disorder with only 41 cases reported in the international literature from 1936 to 2009. The occurrence of syngnathia without any other associated systemic disease or congenital anomaly is extremely rare. This report presents a case of congenital syngnathia with unilateral maxillomandibular bony adhesion without any other oral or maxillofacial anomaly. No recommended protocol for surgery exists due to the rarity of the disorder. There is a very low survival rate for the few patients who have forgone surgical management. This case describes a 74-year-old female patient who was suffering from limitation of mouth opening and was subsequently diagnosed with congenital syngnathia. The surgical staff performed separation surgery and reconstructed the malformed oral vestibule and cheek using the radial forearm free flap operation.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Estresse Psicológico
/
Sinostose
/
Bochecha
/
Taxa de Sobrevida
/
Retalhos de Tecido Biológico
/
Antebraço
/
Anormalidades Maxilomandibulares
/
Boca
Tipo de estudo:
Guia de Prática Clínica
Limite:
Idoso
/
Feminino
/
Humanos
Idioma:
Inglês
Revista:
Journal of the Korean Association of Oral and Maxillofacial Surgeons
Ano de publicação:
2012
Tipo de documento:
Artigo
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