Supraventricular tachycardia in a neonate with cardiac rhabdomyoma and tuberous sclerosis / 소아과
Korean Journal of Pediatrics
;
: 766-770, 2008.
Artigo
em Inglês
| WPRIM
| ID: wpr-153556
ABSTRACT
Primary tumors of the heart are uncommon among pediatric patients. Rhabdomyoma is the most frequent cardiac tumor in infants and children, which is commonly associated with tuberous sclerosis. Tuberous sclerosis is a neurocutaneous syndrome affecting the brain, heart, skin, and other organs. Cardiac rhadomyomas are reported in 50-64% of infants with tuberous sclerosis. Tuberous sclerosis involves multiple locations in the atrium, ventricle and septum, and may induce mechanical obstruction of the outflow tract and heart failure depending on the location, number, size, and degree of invasion of tumors. Arrhythmias may also develop in infants with cardiac rhadomyomas, but only a few of these patients require prolonged anti-arrhythmic therapy because arrhythmia often disappears with spontaneous regression of the tumors, and the ultimate prognosis may be decided by the cerebral manifestations.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Arritmias Cardíacas
/
Prognóstico
/
Rabdomioma
/
Pele
/
Esclerose Tuberosa
/
Taquicardia Supraventricular
/
Encéfalo
/
Síndromes Neurocutâneas
/
Coração
/
Insuficiência Cardíaca
Tipo de estudo:
Estudo prognóstico
Limite:
Criança
/
Humanos
/
Lactente
/
Recém-Nascido
Idioma:
Inglês
Revista:
Korean Journal of Pediatrics
Ano de publicação:
2008
Tipo de documento:
Artigo
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