A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 90-94, 2015.
Artigo
em Inglês
| WPRIM
| ID: wpr-157435
ABSTRACT
Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Osteólise
/
Prognóstico
/
Insuficiência Respiratória
/
Costelas
/
Esqueleto
/
Esterno
/
Tórax
/
Reabsorção Óssea
/
Quilotórax
/
Doenças Raras
Tipo de estudo:
Estudo prognóstico
Limite:
Adolescente
/
Humanos
/
Masculino
Idioma:
Inglês
Revista:
The Korean Journal of Thoracic and Cardiovascular Surgery
Ano de publicação:
2015
Tipo de documento:
Artigo
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