A case of idiopathic pulmonary hemosiderosis with seasonal recurrence / 소아과
Korean Journal of Pediatrics
;
: 256-260, 2009.
Artigo
em Inglês
| WPRIM
| ID: wpr-157905
ABSTRACT
Idiopathic pulmonary hemosiderosis (IPH) is a rare disease affecting mostly children. This disorder is characterized by recurrent episodes of hemoptysis, bilateral diffuse pulmonary infiltrates, and iron-deficiency anemia. An acute fulminant alveolar hemorrhage can be fatal due to respiratory failure, while chronic hemorrhage leads to hemosiderin-laden macrophages and pulmonary fibrosis. Genetic, autoimmune, allergic, environmental, and metabolic mechanisms of pathogenesis have been suggested, but the etiology of IPH remains unknown. We report on a 9-year-old girl with idiopathic pulmonary hemosiderosis who showed seasonal recurrences without cause.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Fibrose Pulmonar
/
Recidiva
/
Insuficiência Respiratória
/
Estações do Ano
/
Anemia Ferropriva
/
Doenças Raras
/
Hemoptise
/
Hemorragia
/
Hemossiderose
/
Pneumopatias
Limite:
Criança
/
Humanos
Idioma:
Inglês
Revista:
Korean Journal of Pediatrics
Ano de publicação:
2009
Tipo de documento:
Artigo
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