Spontaneous aortic rupture in a patient with neurofibromatosis type 1 / 대한외과학회지
Journal of the Korean Surgical Society
;
: 261-265, 2012.
Artigo
em Inglês
| WPRIM
| ID: wpr-15803
ABSTRACT
Neurofibromatosis type I (NF-1) is a rare autosomal dominant genetic disorder occurring in 1 in 3,000 individuals. Vasculopathy is a rarely reported finding in patients with NF-1. Here, we report a case of recurrent aortic pseudoaneurysm after endovascular aneurysm repair in a 49-year-old male patient with NF-1. On the sixth postoperative day following a successful open surgical repair of an aortic pseudoaneurysm, he developed hemoperitoneum due to a delayed rupture of the mesenteric artery branch. This was treated with endovascular coil embolization. We report the clinical features and histologic findings of this rare vascular disorder with a review of the relevant literature.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Aneurisma Aórtico
/
Ruptura Aórtica
/
Ruptura
/
Neurofibromatose 1
/
Neurofibromatoses
/
Falso Aneurisma
/
Hemoperitônio
/
Aneurisma
/
Artérias Mesentéricas
Limite:
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Journal of the Korean Surgical Society
Ano de publicação:
2012
Tipo de documento:
Artigo
Similares
MEDLINE
...
LILACS
LIS