Single Lung Transplantation in the Patient with End-stage Lymphangioleiomyomatosis: Report of 1 case / 대한흉부외과학회지
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 1015-1018, 2004.
Artigo
em Coreano
| WPRIM
| ID: wpr-158779
ABSTRACT
Lymphangioleiomyomatosis (LAM) is a rare disease in women in childbearing age leading to progressive respiratory failure. LAM is characterized by an abnormal harmartomatous proliferation of smooth muscle cells surrounding the blood vessels, lymphatics and airways in the lung. This proliferation leads to airway obstruction, cystic alveolar change and lymphatic obstruction. Patients present with dyspnea, pneumothorax, cough, chest pain, hemoptysis, and chylous effusion. Although lung transplantation is the only therapeutic modality in end-stage LAM with respiratory failure, there has not been any report of successful treatment in Korea. We report one case of successful left single lung transplantation in a 40 year old woman suffering from end-stage LAM.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Pneumotórax
/
Insuficiência Respiratória
/
Vasos Sanguíneos
/
Dor no Peito
/
Transplante de Pulmão
/
Linfangioleiomiomatose
/
Tosse
/
Miócitos de Músculo Liso
/
Doenças Raras
/
Obstrução das Vias Respiratórias
Limite:
Adulto
/
Feminino
/
Humanos
País/Região como assunto:
Ásia
Idioma:
Coreano
Revista:
The Korean Journal of Thoracic and Cardiovascular Surgery
Ano de publicação:
2004
Tipo de documento:
Artigo
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