Surgical Treatment of Congenital Cystic Lung Disease / 대한흉부외과학회지

ABSTRACT

BACKGROUND: Congenital cystic diseases of the lung are uncommon but they share similar embryogenic and clinical characteristics. MATERIAL AND METHOD: From 1972 to 1999, 46 patients were operated on in the Dept. of Thoracic Surgery at the YUMC. And we analysed the patients' charts for clinical presentations, managements and pathologic findings with chart of patients. RESULT: There were 17 males and 29 females, and mean age was 16.2 years. The main symptoms were 11 fevers due to recurrent infection, 10 dyspneas, and chest pain and sputum production etc. Thirteen patients were asymptomatic. There were 13 pulmonary sequestrations(PS), 12 congenital cystic adenomatoid malformations(CCAM), 12 bronchogenic cysts(BC), 5 cystic bronchiectasis(CB) and 4 congenital lobar emphysemas(CLE). Simple excision(resection) was performed in 8 patients, segmentectomy in 6 patients, lobectomy (with 1 operative mortality) in 31 patients, and pneumonectomy in one patient. The compli-cations were 4 pneumonias, one persistent air leakage and one empyema. CONCLUSION: We experienced surgical treatment of congenital cystic lung disease and reported them with literature review.