A Case of Peutz-Jeghers Syndrome with Small Bowel Neuroendocrine Carcinoma / 대한내과학회지
Korean Journal of Medicine
;
: 698-703, 2013.
Artigo
em Coreano
| WPRIM
| ID: wpr-162104
ABSTRACT
Peutz-Jeghers syndrome (PJS) is an autosomal dominant inherited disorder characterized by hamartomatous polyps in the gastrointestinal tract and mucocutaneous melanin pigmentation. Hamartomas are not generally regarded as premalignant, although patients with PJS are at increased risk for common and unusual types of gastrointestinal and non-gastrointestinal malignancies. However, most of the reported gastrointestinal malignancies have been adenocarcinomas, and few reports of an association of this syndrome with a neuroendocrine tumor (NET) have been published. Moreover, no case of this syndrome with NET has been reported in Korea. Here, we report a 21-year old male with PJS who had a small bowel neuroendocrine carcinoma.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Pólipos
/
Pigmentação
/
Síndrome de Peutz-Jeghers
/
Adenocarcinoma
/
Tumores Neuroendócrinos
/
Carcinoma Neuroendócrino
/
Trato Gastrointestinal
/
Hamartoma
/
Coreia (Geográfico)
/
Melaninas
Limite:
Humanos
/
Masculino
País/Região como assunto:
Ásia
Idioma:
Coreano
Revista:
Korean Journal of Medicine
Ano de publicação:
2013
Tipo de documento:
Artigo
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