A Typical Korean Case Of Carney Complex
The Korean Journal of Internal Medicine
;
: 260-265, 2003.
Artigo
em Inglês
| WPRIM
| ID: wpr-163940
ABSTRACT
Carney complex is a multiple neoplasia syndrome, inherited in an autosomal dominant manner, that is characterized by lentigines, cardiac myxoma, and numerous endocrine and other tumors, including primary pigmented nodular adrenocortical disease. Here, we describe a typical case of Carney complex in a 27- year-old female who exhibited spotty skin pigmentation on the lips, oral mucosa, fingers, and toes and several manifestations of Cushing's syndrome due to primary pigmented nodular adrenocortical disease. She also had pituitary adenoma, breast tumor and thyroid nodule. Only a few cases of this disorder have been reported in the Korean literature. All of them, however, had only two components of Carney complex composed of skin pigmentation and primary pigmented nodular adrenocortical disease. Therefore, the present case seems to be the first true case of Carney complex reported in Korea.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Neoplasias Hipofisárias
/
Neoplasias Cutâneas
/
Síndrome
/
Neoplasia Endócrina Múltipla
/
Imageamento por Ressonância Magnética
/
Hiperpigmentação
/
Síndrome de Cushing
/
Mixoma
/
Neoplasias Primárias Múltiplas
Limite:
Adulto
/
Feminino
/
Humanos
Idioma:
Inglês
Revista:
The Korean Journal of Internal Medicine
Ano de publicação:
2003
Tipo de documento:
Artigo
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