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Scoliosis Associated with Marfan Syndrome / 대한척추외과학회지
Journal of Korean Society of Spine Surgery ; : 482-490, 2001.
Artigo em Coreano | WPRIM | ID: wpr-16888
ABSTRACT

OBJECTIVES:

To evaluate characteristics and results of treatment of scoliosis associated with Marfan syndrome

METHODS:

The clinical data of 57 patients diagnosed as Marfan syndrome from January 1989 to June 1999 were reviewed. Thirty one patients had major curves more than 10 degrees by Cobb's method on whole spine standing film and their curve patterns and treatment methods were analyzed. Twelve cases of Marfan scoliosis who underwent posterior instrumented fusion were compared with randomly-sampled cases with idiopathic scoliosis about flexibility, correctability and correction loss of curves.

RESULTS:

Scoliosis was identified in 31 of 57 patients (54.4%) and among them 15 patients had the curve more than 40 degrees. Twelve curves were double major, 10 were thoracic, and 8 were double thoracic. Seventy-five per cent of the 57 patients had congenital heart disease and 40% had lens dislocation. Twelve of 31 cases underwent posterior fusion with pedicle screw instrumentation. Marfan scoliosis (mean flexibility; 39% in thoracic, 52% in lumbar) were significantly less flexible than idiopathic scoliosis (60% in thoracic, 93% in lumbar) (P0.05). Mean correction loss in Marfan syndrome was 3.2% at the mean 4.1 year follow-up in 9 cases.

CONCLUSIONS:

The prevalence of scoliosis in Marfan syndrome shows positive correlation with severity of the disease. As compared to idiopathic scoliosis, the curve associated with Marfan syndrome was larger and less flexible. After posterior fusion using pedicle screw instrumentation, the correctability of Marfan curve was poorer than that of idiopathic curve, which is, however, insignificant statistically. So it was considered to be a good method to treat Marfan scoliosis.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Escoliose / Coluna Vertebral / Subluxação do Cristalino / Prevalência / Seguimentos / Maleabilidade / Cardiopatias Congênitas / Síndrome de Marfan Tipo de estudo: Estudo observacional / Estudo de prevalência / Estudo prognóstico / Fatores de risco Limite: Humanos Idioma: Coreano Revista: Journal of Korean Society of Spine Surgery Ano de publicação: 2001 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Escoliose / Coluna Vertebral / Subluxação do Cristalino / Prevalência / Seguimentos / Maleabilidade / Cardiopatias Congênitas / Síndrome de Marfan Tipo de estudo: Estudo observacional / Estudo de prevalência / Estudo prognóstico / Fatores de risco Limite: Humanos Idioma: Coreano Revista: Journal of Korean Society of Spine Surgery Ano de publicação: 2001 Tipo de documento: Artigo