Recurrent Massive Subcutaneous Hemorrhage in Neurofibromatosis Type 1: A Case Report
Journal of Korean Medical Science
; : 728-730, 2007.
Article
em En
| WPRIM
| ID: wpr-169941
Biblioteca responsável:
WPRO
ABSTRACT
Neurofibromatosis type 1 (NF-1) is an autosomal dominant disorder that has three major features: multiple neural tumors, cafe-au-lait spots, and pigmented iris hamartomas (Lisch nodules). The purpose of this case report is to advise physicians of the danger associated with the progression of fast-onset massive hemorrhage to hemodynamic instability, which mandates rapid treatment to prevent the development of a life-threatening condition. A 64-yr-old woman with NF-1 was admitted to the Emergency Department (ED) because of a rapidly growing, 10x5x3 cm-sized mass on the left back area. She had previously undergone surgery for a large subcutaneous hematoma, which had developed on her right back area 30 yr before. She became hemodynamically unstable with hypotension during the next 3 hr after admission to ED. Resuscitation and blood transfusion were done, and the hematoma was surgically removed. The mass presented as a subcutaneous, massive hematoma with pathologic findings of neurofibroma. We report a case of NF-1 that presented as recurrent, massive, subcutaneous hemorrhage on the back region combined with hypovolemic shock.
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Texto completo:
1
Índice:
WPRIM
Assunto principal:
Recidiva
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Dermatopatias
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Tomografia Computadorizada por Raios X
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Neurofibromatose 1
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Diagnóstico Diferencial
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Hematoma
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Hemorragia
Tipo de estudo:
Diagnostic_studies
Limite:
Female
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Humans
Idioma:
En
Revista:
Journal of Korean Medical Science
Ano de publicação:
2007
Tipo de documento:
Article