Abdominal Aortic Aneurysm in Marfan's Syndrome: Two Cases
Journal of the Korean Society for Vascular Surgery
;
: 30-34, 2006.
Artigo
em Coreano
| WPRIM
| ID: wpr-171387
ABSTRACT
Marfan syndrome is an inherited autosomal dominant disorder of the connective tissues, and the afflicted patients present with abnormalities of the skeletal, ocular, and cardiovascular system. The progressive dilatation of the proximal aorta leading to dissection and rupture is the typical feature and this can be a lethal complication of this disease. The incidence of Marfan syndrome is estimated to be 1 in 10,000 in most racial and ethnic groups. We experienced two cases of aortic aneurysm in Marfan syndrome. The first case was 32-year-old woman. She was admitted because of sudden onset of a painful abdominal mass for 2 days. Aortic aneurysm was diagnosed by CT and an echocardiogram showed severe mitral regurgitation (area ratio 13/15). She underwent successful abdominal aortic aneurysm (AAA) repair and was discharged on postoperative 14th day; she was then prepared for open cardiac surgery for mitral valve replacement. The second case was 19- year-old woman. She was admitted with a known abdominal aortic aneurysm that she'd had for 1.5 years. She also underwent abdominal aortic aneurysm (AAA) repair that was technically successful, but she died on postoperative 10th day due to sudden cardiac arrest.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Aorta
/
Aneurisma Aórtico
/
Ruptura
/
Cirurgia Torácica
/
Sistema Cardiovascular
/
Etnicidade
/
Incidência
/
Morte Súbita Cardíaca
/
Aneurisma da Aorta Abdominal
/
Tecido Conjuntivo
Tipo de estudo:
Estudo de incidência
/
Estudo prognóstico
Limite:
Adulto
/
Feminino
/
Humanos
Idioma:
Coreano
Revista:
Journal of the Korean Society for Vascular Surgery
Ano de publicação:
2006
Tipo de documento:
Artigo
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