A Case of Juvenile Onset Lennox-Gastaut Syndrome Presenting as Atypical Absence / 대한간질학회지
Journal of Korean Epilepsy Society
;
: 147-149, 2002.
Artigo
em Coreano
| WPRIM
| ID: wpr-173983
ABSTRACT
Atypical absence is less understood than typical absence. Several conditions that produce atypical absence are known including Lennox-Gastaut syndrome, myoclonic astatic epilpsy and epileptic encephalopathy with continuous spike and waves in slow wave sleep. A 17-year-old girl with mental retardation had developed frequent loss of consciousness and occasional falling attack with traumatic facial injury for 2 years. The interictal EEG showed 2 Hz slow spike-and-wave complex with maximum over right frontotemporal area and the brain MRI was normal. Carbamazepin was prescribed initially but the drug seemed to worsen the seizures. Long term video-EEG monitoring showed very frequent atypical absence seizures consisting of sudden hypotonia of head and oral automatism with or without secondary generalization. Generalized 2 to 2.5 Hz slow spike-and-wave complexes with duration of 10 to 40 seconds were seen during ictal period. About 10% to 20% of the non REM sleep was occupied with generalized slow spike-and-wave complex and/or polyspikes or polyspikes-and-wave complex with duration of within 1 second. Valprorate monotherapy had failed, then lamotrigin was added. In spite of polytherapy, the seizure was intractable. We think this intractable atypical absence might be associated with juvenile onset Lennox-Gastaut syndrome.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Convulsões
/
Sono REM
/
Automatismo
/
Inconsciência
/
Encéfalo
/
Imageamento por Ressonância Magnética
/
Epilepsia Tipo Ausência
/
Eletroencefalografia
/
Traumatismos Faciais
/
Generalização Psicológica
Limite:
Adolescente
/
Feminino
/
Humanos
Idioma:
Coreano
Revista:
Journal of Korean Epilepsy Society
Ano de publicação:
2002
Tipo de documento:
Artigo
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