Anesthetic Experience of the Patient with Nemaline Myopathy: A case report / 대한마취과학회지

ABSTRACT

Nemaline rod myopathy is an autosomal dominant disease characterized by nonprogressive symmetric skeletal muscle weakness affecting principally proximal skeletal muscles. Anesthesia of the patient with this disease is known to present some problemsdifficult intubation due to facial dysmorphism, delayed onset of succinilcholine, reduced vital capacity on pulmonary function test and skeletal deformity. We anesthetized 19 year old male patient with nemaline myopathy for the operation of cryptochidism. Because of the possibility of difficult intubation, we produced epidural anesthesia with 20 G Tuohy needle at L5-S1 intervertebral space successfully. There were no problems in the course of operation and recovery except transient airway obstruction due to sedative.