A Case of Congenital Long QT Syndrome Associated with Deafness and Syncope
Korean Circulation Journal
;
: 1882-1888, 1998.
Artigo
em Coreano
| WPRIM
| ID: wpr-179386
ABSTRACT
Congenital long QT syndrome (LQTS) is an inherited disease characterized by prolonged QT intervals and polymorphic ventricular tachycardia. The clinical manifestations vary from sudden cardiac death by ventricular arrhythmia to asymptom throughout life. In 1957, Jervell and Lange-Nielsen reported a syndrome of congen-ital sensory deafness associated with a prolonged QT interval in four children. The affected children had multiple syncopal episodes, and three died suddenly. The mode of inheritance is autosomal recessive. Affected persons are susceptible to recurrent syncope, and they have a high incidence of sudden death and short life expectancy. We report a case and review the literature on long QT syndrome diagnosed in a 30-year-old female with a history of convulsion and loss of consciousness during delivery.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Arritmias Cardíacas
/
Convulsões
/
Síncope
/
Inconsciência
/
Testamentos
/
Síndrome do QT Longo
/
Incidência
/
Expectativa de Vida
/
Morte Súbita Cardíaca
/
Taquicardia Ventricular
Tipo de estudo:
Estudo de incidência
/
Estudo prognóstico
Limite:
Adulto
/
Criança
/
Feminino
/
Humanos
Idioma:
Coreano
Revista:
Korean Circulation Journal
Ano de publicação:
1998
Tipo de documento:
Artigo
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